Comprehensive Pediatric Sickle Cell Program



This is a nationally recognized program which has been the recipient of competitive grants from the Health Resources and Service Administration since 1995. The Program is enhanced by funding from New York State Department of Health.

Board Certified Hematologists and other personnel provide coordinated care in all settings.



Our Mission


Our mission is to provide coordinated, comprehensive medical care, education and psychosocial support to enhance quality of life of patients with sickle cell disease and their families.


Services


  • Evaluation and genetic counseling for all patients

  • 24 hour urgent care

  • State of the art patient care Pain management

  • Trans-Cranial Doppler (TCD) screening for stroke

  • Phenotype matched transfusions

  • Coordination of multi-disciplinary care

  • Support groups for parents and young adults

  • Patient, professional and community education

  • Quarterly Newsletter - The Sickle Star


For more information please contact: (718) 240-5904



Facts About Sickle Cell Disease



What is Sickle Cell Disease?


Sickle cell disease is a genetic condition that causes a lifelong anemia (low blood count). This happens because of a change in the makeup of the heamoglobin (a protein in the red blood cells) which carries oxygen to the body.


What happens with Sickle Cell Disease?


Normal red blood cells are shaped like a doughnut which allows them to squeeze through small blood vessels. In sickle cell disease, red blood cells are sickle shaped, unbending and block small blood vessels. They also break up easily and causes anemia. Major complications are painful crises, serious infection, stroke and damage to body organs


sickle cell

How common is Sickle Cell Disease?


Sickle cell disease affects millions of people worldwide. It affects over 100,000 people in the U.S.


  • Is most common among people of African descent. 1 in every 12 African Americans has the trait. 1 in every 400 has sickle cell disease.
  • It also affects people from Spanish speaking regions (South and Central America, Cuba). 1 in every 100 Hispanics has the trait. 1 in every 1000 Hispanics has sickle cell disease.
  • It also affects people from another regions; India, Saudi Arabia and the Mediterranean (Italy, Greece, Turkey).

Types of Sickle Cell Disease?


There are several types of sickle cell disease. The most common are:


  • Sickle Cell Anemia (SS)
  • Sickle C Disease (SC)
  • Sickle Beta-Plus Thalassemia (SB+)
  • Sickle Beta-Zero Thalassemia (SBO)

How do you get Sickle Cell Disease?


sickle cell

If both mother and father carry the trait for a sickle cell disorder, there is a:


  • 25% chance with each pregnancy for that child to have sickle cell disease.
  • 50% chance for the child to have a trait
  • 25% chance that the child will not have disease or trait.

What medical problems are associated with Sickle Cell Disease?


In sickle cell disease, hemoglobin, a component of red blood cells that carries oxygen is altered. This causes the red blood cells to stiffen and twist into jagged “sickle” shapes. These cells block small blood vessels leading to:



Are children at serious risk?


Children with sickle cell disease are more likely to get severe bacterial infections and sudden enlargement of the spleen.
Click here to know more


How do you test for Sickle Cell?


A blood test called hemoglobin electrophoresis will detect sickle cell disease, trait and other hemoglobin types.


What is Sickle Cell Trait?


Sickle cell trait (AS) is an inherited condition where one carries the gene for sickle cell.People with sickle cell trait are generally healthy but should be aware of their trait status.

Click for more information on Sickle Cell Trait


Special Treatments


Treatments such as blood transfusions, Transcranial doppler testing and special medications which may require close observation during administration are given in our office or in our Ambulatory Infusion/Therapy Unit (AITU) which has a dedicated staff. We also work closely with the Department of Anesthesiology's Pain Management Center to design individual treatment plans. Maintaining our patient's comfort and integrity is our primary responsibility.


Contact


The Brookdale University Hospital and Medical Center


Division of Pediatric Hematology/Oncology
One Brookdale Plaza
Suite 346 CHC
Brooklyn, NY 11212-3198

Phone: (718) 240-5904

Fax: (718) 240-6730

Emergency Beeper Number
(917) 433-7764